Hypoparathyroidism as the First Mani-Festation of Kearns-Sayre Syndrome: A Case Report

Authors

  • Farah Ashrafzadeh Professor of pediatric neurology, Ghaem Medical Center, Mashhad, Iran
  • Javad Akhondian Professor of pediatric neurology, Ghaem Medical Center, Mashhad, Iran
  • Mehran Beiraghi Toosi Fellowship of Pediatric Neurology, Medical Center, Mashhad, Iran
  • Nosrat Ghaemi Professor of Pediatric Endocrinology, Imam Reza Center, Mashhad, Iran
  • Saghi Elmi Pediatrician, Ghaem Medical Center, Mashhad, Iran
Abstract:

Kearns-Sayre syndrome is a mitochondrial myopathy, which was first described by Tomas Kearn in 1958. Diagnostic symptoms of this condition include retinitis pigmentosa, chronic progressive external ophthalmoplegia, and one or more of the following factors: cardiac conduction system diseases, cerebellar ataxia, and cerebrospinal fluid (CSF) with protein content above 100 mg/dL. The nature of this uncommon disease is yet to be clarified. According to previous reports, it is uncommon to see hypoparathyroidism as the first manifestation of Kearns-Sayre syndrome. Herein, we report a case of Kearns-Sayre syndrome, with hypoparathyroidism as the first manifestation.

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Journal title

volume 5  issue Abstract

pages  2- 2

publication date 2014-10-01

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